Presentation of large vestibular aqueduct syndrome to a dizziness unit

An abnormally enlarged vestibular aqueduct has been associated with sensorineural hearing loss in children. Vestibular complaints, in this patient population, have not been characterized. Several patients have presented to the dizziness unit at Sunnybrook with vestibular related complaints. These patients all had sensorineural hearing loss noted in childhood. All provided recollections of periods of imbalance and vertigo. High resolution CT scan documented the presence of bilateral enlarged vestibular aqueducts. The Large Vestibular Aqueduct Syndrome (LVAS) will be discussed with reference to the pathophysiology of the vestibular complaints.