Primary mantle cell lymphoma of the trachea

Primary mantle cell lymphoma (MCL) is a controversial entity. It is difficult to diagnose MCL in a single organ without lymph node involvement. However, with the advent of PET-CT scans and large panels of immunohistochemistry markers, there have been increasing reports of primary MCL detected in various organs of which the GI tract is the most common. In this case report, we describe the diagnosis and clinical course of a patient who presented with B symptoms and respiratory distress. On further investigation, he was found to have a mass in his trachea, which was diagnosed as primary MCL.